Résumé
Lymphangioma circumscriptum (LC) is a rare benign disorder of lymphatic channels in deep dermal and subcutaneous layers. Typically fluid filled vesicles that contain lymphatic fluid with frogspawn-like appearance are seen over any part of body. Vulvar LC is seen as congenital condition or might develop secondary to radiotherapy or surgery. LC involving the vulva is very rare; only 33 cases of vulvar LC have been reported. Surgical treatment is the most commonly used method to treat vulvar LC. In this report we present a case with LC secondary to radiotherapy and lesions regressed with cryotherapy.
Sujets)
Adulte , Femelle , Humains , Lymphangiome/anatomopathologie , Lymphangiome/chirurgie , Tumeurs de la vulve/anatomopathologie , Tumeurs de la vulve/chirurgieRésumé
Systemic sclerosis is unusual in childhood. Two cases who presented with diffuse hidebound skin associated with gastrointestinal and pulmonary abnormalities are described here