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Acta Academiae Medicinae Sinicae ; (6): 617-620, 2016.
Article Dans Anglais | WPRIM | ID: wpr-277930

Résumé

Eosinophilic granulomatosis with polyangiitis(EGPA),also known as Churg-Strauss syndrome,is a clinically rare small-vessel vasculitis associated with antineutrophil cytoplasmic antibodies (ANCAs) and the hypereosinophilic syndromes (HESs),characterized by asthma,disseminated necrotizing vasculitis,extravascular granulomas,peripheral eosinophilia,and tissue eosinophilia. This article reviews the pathology,imaging,and clinical features of EGPA.


Sujets)
Humains , Anticorps anti-cytoplasme des polynucléaires neutrophiles , Asthme , Syndrome de Churg-Strauss , Diagnostic , Anatomopathologie , Éosinophilie , Granulomatose avec polyangéite , Diagnostic , Anatomopathologie
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