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Indian Pediatr ; 2009 Apr; 46(4): 354-6
Article Dans Anglais | IMSEAR | ID: sea-8282

Résumé

Juvenile Pagets disease (JPD), a rare genetic disorder characterized by markedly accelerated bone turnover, presents in early childhood. We report a child with typical features of JPD who remained undiagnosed till 15 years of age. Rarity of this disease in Indian literature and need for early diagnosis to prevent progression of disease prompted us to report this case.


Sujets)
Adolescent , Humains , Mâle , Maladie de Paget des os/complications , Maladie de Paget des os/diagnostic , Maladie de Paget des os/thérapie
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