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Article Dans Anglais | IMSEAR | ID: sea-65618

Résumé

Penicillamine is the standard therapy for Wilson's disease in children. We report an 8-year-old-girl with liver disease due to Wilson's disease who developed extrapyramidal symptoms following administration of penicillamine. Symptoms resolved within 20 hours of stopping the drug but recurred within 24 hours when gradually increasing small doses were recommenced.


Sujets)
Chélateurs/effets indésirables , Enfant , Relation dose-effet des médicaments , Femelle , Dégénérescence hépatolenticulaire/traitement médicamenteux , Humains , Maladies neurodégénératives/induit chimiquement , Pénicillamine/effets indésirables , Syndrome
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