Advances on ANCA-associated vasculitis / 复旦学报（医学版）

Antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) consists of autoimmune diseases characterized by necrotizing inflammation of small vessels and presence of ANCA.As a kind of life-threatening disease,AAV tends to involve a plenty of systems,and is subject to relapse even after complete remission.In this review,we focus on the latest progress of epidemiology,etiology,pathogenesis and clinical diagnosis of AAV.