RÉSUMÉ
Papular acantholytic dermatosis localized to the anogenital area is clinically characterized by discrete and grouped papules confined to the anogenital area. Histologically, it shows suprabasal acantholysis resembling that observed in familial benign chronic pemphigus or Darier's disease. However, lack of family history and characteristic skin lesions at other body sites help to distinguish it from those conditions. We describe a 53-year-old woman with unusual asymptomatic, grouped papular lesions on the left perianal area, resembling lichen planus, clinically and familial benign chronic pemphigus, histologically. We think the findings of our patient may represent a distinct acantholytic eruption that should be distinguished from other generalized blistering acantholytic dyskeratotic disorders that may also involve the anogenital area.