Abdominal Aortic Hypoplasia, a Rare Cause of Hypertension.

Hypoplasia of the abdominal aorta is an exceedingly rare vascular abnormality. Congenital, acquired, infectious and inflammatory etiologies have been described. Hypertension is the most common presenting symptom. Besides hypertension, lower extremity claudication and mesenteric ischemia can be seen. Symptoms typically occur within the first three decades of life. Hypoplasia of the abdomanial aorta is considered a life threatening condition as a result of complications associated with severe hypertension. In this article we present a hypertensive patients with hypertrophic left heart, dilation of the ascending aorta and the aortic root, hypoplastic stenosis of the abdominal aorta, celiac trunc, and the places of origin of superior mesenteric and renal arteries and arch of Riolan (collaterals between the mesenteric arteries). Abdominal aortic hypoplasia is presented as a rare cause of hypertension.

A Case of Unusual Form of Williams Syndrome

Williams syndrome is a progressive and multisystemic disorder. We experienced one case of Willams syndrome which was characterized by elfin facies, mental retardation, diffuse aortic hypoplasia, mitral regurgitation and chronic nonparoxysmal sinus tachycardia. The tachycardia has been managing with beta-blocker successfully. We presented a case of unusual form of Williams syndrome with a reivew of literatures.