Résumé
Cystic lymphangiomas are rare neoplasms. A 49 year old male patient presented with complaints of lump in abdomen weight loss since 1 month. On examination, patient had a diffuse visible lump above the umbilicus. Ultrasonography of abdomen and pelvis showed a well-defined smoothly marginated anechoic to hyperechoic lesion in midline and left side of abdomen. CECT of abdomen and pelvis was suggestive of pedunculated small bowel leiomyoma desmoid tumor. Exploratory laparotomy with resection of affected loop of jejunum and the supplying mesentery containing the tumor and resection and anastomosis of adjacent small bowel was done. Histologically, the tumor was diagnosed as mesenteric lymphangioma.
Résumé
Mesenteric lymphangiomas, which involve near total mesentery, are extremely rare. A mesenteric lymphangioma should be treated through excision because they can cause invasion of vital structures, bleeding, or infection. After excision of a huge mesenteric lymphangioma, internal herniation may occur through a large mesenteric defect leading to intestinal volvulus, obstruction, and other life-threatening circumstances. We report a case in which a biologic collagen implant (Permacol) was used for mesenteric defect repair after excision of a huge mesenteric lymphangioma. The implant did not cause any symptoms or complications during follow-up for 4 years. When encountering large defects of mesentery, closure with implant can be a feasible choice, and Permacol could be a possible implant for closing the defect.
Sujets)
Enfant , Humains , Collagène , Études de suivi , Hémorragie , Volvulus intestinal , Lymphangiome , MésentèreRésumé
Mesenteric lymphangioma, which is rare and often diagnosed incidentally, is a benign tumor in infants and children. Most cases of lymphangioma are in the neck and axilla. About 5% of these lesions are in the mediastinum, mesentery or retroperitoneal region. Although most lymphangioma produce no symptoms, it may present an acute surgical condition suggesting acute intestinal obstruction. We report one case of histologically confirmed mesenteric lymphangioma causing billous vomiting and bloody stool in a 3-day-old infant.
Sujets)
Enfant , Humains , Nourrisson , Aisselle , Occlusion intestinale , Lymphangiome , Médiastin , Mésentère , Cou , VomissementRésumé
Mesenteric lymphangioma was first recognized when an autopsy case was recorded in 1507 by Benevieni. It has been known clinically rare disease and probably a congenital developmental abnormality due to failure of drainage of peripheral primary lymphatic spaces. We experienced a case of abnormal rotation in intestine by mesenteric lymphangioma in a 8 years old male who showed vomiting and abdominal pain. A brief review of related literatures is also presented.