Résumé
Primary cardiac angiosarcoma is a rare and rapidly progressing tumor characterized by high predilection for right-sided heart involvement and a very poor prognosis. In this report, we present a case of angiosarcoma involving right atrium and ventricle in 61-year old woman with clinical presentation of repeated bloody pericardial effusion. Right atrial perforation was confirmed by contrast echocardiography using hand-agitated saline contrast. Primary cardiac angiosarcoma was confirmed by histological and immunohistochemical studies.
Sujets)
Femelle , Humains , Échocardiographie , Coeur , Atrium du coeur , Hémangiosarcome , Épanchement péricardique , PronosticRésumé
Primary cardiac malignancy is very rare. Angiosarcoma is the most frequent malignant cardiac tumor and associated with a very unfavourable outcome. We report the case of an cardiac angiosarcoma complicated with cardiac tamponade revealed by echocardiography with pericardiocentesis and confirmed histopathologically in a 25 years old man.
Sujets)
Adulte , Humains , Tamponnade cardiaque , Échocardiographie , Tumeurs du coeur , Hémangiosarcome , PéricardiocentèseRésumé
Primary tumors of the heart are rare and the most are benign. Malignant tumors constitute less than 25% of primary cardiac tumors and angiosarcomas are the most commonly reported histologic type. At least 160 cases have been reported in the world, but no previous report in Korea. We reported a case of primary cardiac angiosarcoma located in right atrium.