RÉSUMÉ
A sclerosing stromal tumor of the ovary (SST) is an extremely rare benign solid ovarian tumor,which is derived from the ovarian stroma and is a distinct subtype of sex cord-stromal tumor.It can not just be diagnosed accurately by routine preoperative physic-chemical examinations and postoperative immunohistochemical examinations.Recently,the application of fine needle aspiration cytology (FNAC) has improved diagnostic accuracy,but the final diagnosis relies on pathological examination.Compared with the traditional way of oophorectomy and salpingo-oophorectomy,the laparoscopic removal of SST will improve future success of pregancy.Besides,SST is an obvious endemic problem.Therefore,an increase in preoperative diagnosis rate of SST can avoid casual extension of resection during surgery and protect patients' fertility.
RÉSUMÉ
Nevoid basal cell carcinoma syndrome is inherited as an autosomal dominant trait with variable expressivity. This is characterized by multiple basal cell carcinomas, skeletal abnormalities, ectopic calcification, palmoplantar pits, central nervous system abnormalities, and multiple odontogenic keratocysts of the jaw. We report a case of nevoid basal cell carcinoma syndrome occurring in 14 year old girl, she had multiple basal cell carcinomas, spina bifida in the cervical vertebrae, forked ribs, hypertelorism, ectopic calcification of falx cerebri, palmoplantar pits, medulloblastoma, meningioma and sclerosing stromal tumor of the ovary. Her father had the same clinical features.