RÉSUMÉ
Syringocystadenoma papilliferum is a rare benign hamartomatous tumor arising from apocrine or eccrine sweat glands with a predilection for head and neck. Here we report a case of a 30 year old female who presented to our opd with a nodule over scalp since birth which turned into a hairless , exophytic pinkish growth with blood tinged discharge slowly over the last 2 years . A punch biopsy of the lesion revealed syringocystadenoma papilliferum. Excision of the lesion is performed and specimen is sent for (hpe) histopathological examination which revealed syringocystadenoma papilliferum with no malignant transformation. Post operative recovery was uneventful and the patient was followed up till 6 months with no history of recurrence.
RÉSUMÉ
Objective:To investigate clinical manifestations and histopathological features of and surgical timing for cerebriform sebaceous nevus.Methods:Clinical data were collected from 14 children with cerebriform sebaceous nevus in Beijing Children′s Hospital from June 2014 to December 2019, and clinical manifestations, histopathological features and surgical timing were analyzed retrospectively.Results:Of the 14 children, 10 were males and 4 were females. They presented with skin lesions at birth, which were solitary and located on the head and face. These skin lesions gave a cerebriform appearance, with an average diameter of 4.79 cm. Systemic examination showed no abnormality in any children. Histopathological examination showed obvious papillomatous epidermal hyperplasia, large number of mature sebaceous glands and immature hair follicles. The 14 children underwent surgeries at an average age of 1.94 years. No recurrence was observed during the follow-up of 6 months to 6 years after surgery.Conclusion:Cerebriform sebaceous nevus is characterized by a unique cerebriform appearance, mostly occurs on the head and face, and is liable to attract attention, which usually leads to an earlier surgical selection.
RÉSUMÉ
Objective To investigate dermoscopic and reflectance confocal microscopic (RCM)features of sebaceous nevus in patients of different ages.Methods A total of 83 patients histopathologically diagnosed with sebaceous nevus were enrolled from Department of Dermatology of Wuhan No.1 Hospital between January 2016 and December 2016,and divided into 4 age groups (＜ 10 years,10-20 years,21-59 years,≥ 60 years) according to the age.The dermoscopic and RCM features were collected and analyzed.Results Among the age group of ＜ 10 years (21 cases),dermoscopic images of skin lesions showed that uniform,globular or plaque-shaped yellowish-red structures arranged in a cobblestone-like pattern were independently distributed in an orange background,with vascular proliferation and dilatation,while RCM images showed sebaceous gland hypoplasia and juvenile hair follicles.Among the age group of 10-20 years (28 cases),dermoscopy showed aggregated,non-hair follicle,round or oval yellow structures of varying sizes with telangiectases,while RCM showed botryoidal sebaceous glands at the dermal-epidermal junction and superficial dermis,which were characterized by tube-like or handle-like structure in the center,aggregated fish roe-like or frogspawn-like sebaceous gland lobules in the surrounding area and verrucous or papillomatous hyperplasia in the epidermis.The age groups of 21-59 years (30 cases) and 10-20 years showed the similar imaging manifestations.The main imaging manifestation of the age group of ≥ 60 years (4cases) was papillomatous hyperplasia.Conclusions Sebaceous nevus is a dynamic developmental disease,and its imaging characteristics obviously differ among different age stages.Sebaceous nevus has characteristic structures under dermoscopy and RCM,which can serve as efficient noninvasive diagnostic methods for sebaceous nevus.
RÉSUMÉ
O nevo sebáceo de Jadassonh é um nevo epidérmico composto por glândulas sebáceas de coloração rosa ou amarelada, que pode apresentar o desenvolvimento de várias neoplasias benignas e malignas. É uma das malformações anexais que ocorre com maior frequência nas crianças1,2. Clinicamente aparece como uma placa bem definida de alopecia no couro cabeludo, face ou colo. Está presente desde o nascimento ou pode surgir alguns anos mais tarde1. Apresentamos o caso de um nevo sebáceo de Jadassohn no couro cabeludo a partir do qual um carcinoma basocelular se desenvolveu e foi diagnosticado com o auxílio da dermatoscopia.
RÉSUMÉ
El nevo sebáceo de Jadassohn es un nevo epidérmico compuesto predominantemente por glándulas sebáceas. Clínicamente se presenta como placas redondas u ovales, de color rosado o a veces amarillento, que se localiza en cuero cabelludo, cara, frente, cuello, tronco o extremidades. Estas lesiones pueden alcanzar gran tamaño y provocan en ocasiones una importante deformidad estética. En estos casos poseen alta incidencia de degeneración maligna.Presentamos este caso debido a lo llamativo del tamaño de la lesión...
Nevus Sebaceous of Jadassohn is a compound epidermal nevus formedpredominantly by sebaceous glands. It presents as round or oval, pinkishor yellow plaque localized to scalp, frontal region, face and neck, trunk andlimbs. NSJ is capable of growing to a considerably size and important estheticimplication.We present this case due to the important extension of the lesion...