RÉSUMÉ
SUMMARY: Situs ambiguous is the placement of vessels and organs in the thoracoabdominal space that are anatomically located outside its normal position in a certain order. This condition is a broad definition that includes many variations. In this case report, we reported a patient with Situs ambiguus with an abnormal hepatic vein who was diagnosed incidentally during medical imaging (computed tomography, sonography and MRI study).
RESUMEN: El Situs ambiguous es la colocación de vasos y órganos en el espacio toracoabdominal que anatómicamente se encuentran fuera de su posición normal en un cierto orden. Esta condición es una definición amplia que incluye muchas variaciones. En este reporte de caso, reportamos un paciente con Situs ambiguous con una vena hepática anormal que fue diagnosticado incidentalmente durante un estudio de imagen médica (tomografía computarizada, ecografía y resonancia magnética).
Sujet(s)
Humains , Femelle , Adulte , Syndrome d'hétérotaxie , Veines hépatiques/malformations , Veines hépatiques/imagerie diagnostiqueRÉSUMÉ
Se comunica la ablación de un flúter auricular con una longitud de ciclo de 260 ms en un paciente de 28 años con isomerismoizquierdo y vena cava inferior izquierda interrumpida. Mediante encarrilamiento, demostramos la participación del istmo suprahepáticotricuspídeoen el circuito de macroreentrada. Realizamos líneas de ablación con radiofrecuencia que detuvieron la arritmia primaria yculminó en ritmo de escape noda.
We report the ablation of an atrial flutter with a 260 ms cycle length in a 28-year-old patient with left isomerism and interrupted leftinferior vena cava. We showed the participation of the suprahepatic tricuspid isthmus in the macro reentry circuit by the entrainmentmaneuver.
Sujet(s)
Humains , Mâle , Adulte , Flutter auriculaire , Cardiopathies congénitales/complications , Isomérie , Veine cave inférieure/anatomopathologie , Présentations de casRÉSUMÉ
Total anomalous systemic venous connection (TASVC) to the left atrium (LA) is a rare congenital anomaly. An 11-year-old girl presented with complaints of palpitations and cyanosis. TASVC with left isomerism and noncompaction of LV was diagnosed after contrast echocardiogram and computed tomography angiogram. The knowledge of anatomy and pathophysiology is essential for the successful management of these cases. Anesthetic concerns in this case were polycythemia, paradoxical embolism and rhythm abnormalities. The patient was successfully operated by rerouting the systemic venous connection to the right atrium.
Sujet(s)
Anesthésie générale/méthodes , Anesthésiques , Troubles du rythme cardiaque/étiologie , Procédures de chirurgie cardiaque/méthodes , Enfant , Thrombose coronarienne/complications , Cyanose/étiologie , Échocardiographie , Femelle , Atrium du coeur/malformations , Atrium du coeur/chirurgie , Ventricules cardiaques/imagerie diagnostique , Humains , Polyglobulie/complications , Prémédication anesthésique , Veines pulmonaires/malformations , Sternotomie , Tomodensitométrie , Veines/malformations , Veine cave supérieure/malformationsRÉSUMÉ
Left isomerism is characterized by bilateral left-sidedness and multiple associated cardiac and visceral anomalies. The clinical manifestation of left isomerism mainly depends upon the cardiac lesions. Occasionally an individual will have a normal heart and be presented with the extracardiac anomalies. A 3-year-old girl with a diagnosis of left isomerism was presented with pulmonary hypertension and intermittent hypoglycemia. Computerized tomography of the abdomen revealed absence of the portal vein and portosystemic shunt. The superior mesenteric and splenic veins joined as a common trunk, bypassed the liver and drained the left renal vein and hemiazygos vein. Her pulmonary hypertension was considered as a consequence of the portosystemic shunt. We report a case of left isomerism in association with absence of the portal vein and a review of literatures.