Résumé
Cor triatriatum é um anomalia cardíaca congênita rara frequentemente diagnosticada na primeira infância. Este estudo de caso apresenta um adulto com um achado acidental de cor triatriatum sinistrum. Com base na apresentação clínica, o paciente foi tratado de forma conservadora. São apresentados achados de imagens ecocardiográficas de cor triatriatum sinistrum deste paciente juntamente de revisão narrativa da literatura sobre essa doença.(AU)
Cor triatriatum is a rare congenital heart anomaly often diagnosed in early childhood. This case study features an adult with an incidental finding of cor triatriatum sinistrum. Based on the clinical presentation, the patient was treated conservatively. Cor triatriatum sinistrum echocardiographic image findings of this patient are presented along with a narrative review of the literature about this disease. (AU)
Sujets)
Humains , Mâle , Adulte d'âge moyen , Coeur triatrial/complications , Coeur triatrial/imagerie diagnostique , Résultats fortuits , Atrium du coeur/malformations , Spectroscopie par résonance magnétique/méthodes , Échocardiographie-doppler/méthodes , Échocardiographie transoesophagienne/méthodes , Échocardiographie tridimensionnelle/méthodes , Stéatose hépatique/complications , Communications interauriculaires/complications , Rein/traumatismes , Infarctus du myocarde/génétiqueSujets)
Adolescent , Procédures de chirurgie cardiaque , Pontage cardiopulmonaire , Sténose pathologique , Coeur triatrial/complications , Coeur triatrial/chirurgie , Coeur triatrial/imagerie diagnostique , Persistance du canal artériel/diagnostic , Persistance du canal artériel/chirurgie , Persistance du canal artériel/imagerie diagnostique , Échocardiographie transoesophagienne , Femelle , Humains , Hypertension pulmonaire/complications , Hypertension pulmonaire/imagerie diagnostique , Surveillance peropératoire , Oxymétrie , Veines pulmonaires/anatomopathologie , Veines pulmonaires/chirurgieRésumé
Pacietne de 16 anos com insuficiência cardíaca e hipertensäo pulmonar, simulando estenose mitral. ecocardiografia bidimensional mostrou valva mitral normal e imagem linear em átrio esquerdo, confirmada à angiografia que evidenciou membrana de cor triatriatum com orifício de 4 mm. Realizou-se ressecçäo cirúrgica da membrana, com bom resultado
A 16-year-old patient was evaluated for congestive heart failure and pulmonary hypertension, suggesting mitral valve stenosis. A left atrial membrane with a 4 mm orifice was seen in echocardiography and angiography, and a diagnosis of cor triatriatum was made. The membrane was successfully removed by surgery
Sujets)
Coeur triatrial/diagnostic , Coeur triatrial/chirurgie , Coeur triatrial/complications , Coeur triatrial , Angiographie , Échocardiographie , Électrocardiographie , Bas débit cardiaque , Cathétérisme cardiaque , Diagnostic différentiel , Hypertension pulmonaire/complications , Défaillance cardiaque/complications , Radiographie thoraciqueRésumé
We report a rare case with a combination of cor-triatriatum, large secundum atrial septal defect and bicuspid aortic valve. The diagnosis was made by cross-sectional echocardiography. A defect was present between proximal (accessory) left atrial chamber and right atrium decompressing the accessory left atrial chamber. The large left to right shunt resulted in severe pulmonary arterial hypertension.
Sujets)
Adulte , Valve aortique/malformations , Coeur triatrial/complications , Échocardiographie , Électrocardiographie , Femelle , Communications interauriculaires/complications , Humains , Hypertension pulmonaire/complicationsRésumé
Un paciente se presentó para examen con tos y hemoptisis y el exámen físico sugirió hipertensión pulmonar. El ecocardiograma división de la auricula izquierda por una membrana, estableciendo el diagnóstico de cor triatriatum. Los hallazgos físicos y del ultrasonido cardiaco se discuten
Sujets)
Adolescent , Humains , Femelle , Coeur triatrial/diagnostic , Échographie , Coeur triatrial/complicationsRésumé
Os autores apresentam um caso de cor triatriatum dexter, diagnosticado por ecodoplercardiografia bidimensional, associado a comuniçäo interatrial e estenose pulmonar valvar. A anomalia näo foi detectada no estudo hemodinâmico. O ecodopplercardiograma mostrou uma ampla membrana dividindo o átrio em duas cavidades, estendendo-se de sua porçäo inferior, imediatamente acima do anel tricúspide, até os orifícios da veias cavas. Esses achados foram confirmados pela necrópsia