Résumé
Cor triatriatum é um anomalia cardíaca congênita rara frequentemente diagnosticada na primeira infância. Este estudo de caso apresenta um adulto com um achado acidental de cor triatriatum sinistrum. Com base na apresentação clínica, o paciente foi tratado de forma conservadora. São apresentados achados de imagens ecocardiográficas de cor triatriatum sinistrum deste paciente juntamente de revisão narrativa da literatura sobre essa doença.(AU)
Cor triatriatum is a rare congenital heart anomaly often diagnosed in early childhood. This case study features an adult with an incidental finding of cor triatriatum sinistrum. Based on the clinical presentation, the patient was treated conservatively. Cor triatriatum sinistrum echocardiographic image findings of this patient are presented along with a narrative review of the literature about this disease. (AU)
Sujets)
Humains , Mâle , Adulte d'âge moyen , Coeur triatrial/complications , Coeur triatrial/imagerie diagnostique , Résultats fortuits , Atrium du coeur/malformations , Spectroscopie par résonance magnétique/méthodes , Échocardiographie-doppler/méthodes , Échocardiographie transoesophagienne/méthodes , Échocardiographie tridimensionnelle/méthodes , Stéatose hépatique/complications , Communications interauriculaires/complications , Rein/traumatismes , Infarctus du myocarde/génétiqueSujets)
Humains , Femelle , Enfant , Coeur triatrial/anatomopathologie , Coeur triatrial/imagerie diagnostique , Veines pulmonaires/malformations , Coeur triatrial/physiopathologie , Échocardiographie , Radiographie thoracique , Électrocardiographie , Atrium du coeur/anatomopathologie , Atrium du coeur/imagerie diagnostiqueSujets)
Adolescent , Procédures de chirurgie cardiaque , Pontage cardiopulmonaire , Sténose pathologique , Coeur triatrial/complications , Coeur triatrial/chirurgie , Coeur triatrial/imagerie diagnostique , Persistance du canal artériel/diagnostic , Persistance du canal artériel/chirurgie , Persistance du canal artériel/imagerie diagnostique , Échocardiographie transoesophagienne , Femelle , Humains , Hypertension pulmonaire/complications , Hypertension pulmonaire/imagerie diagnostique , Surveillance peropératoire , Oxymétrie , Veines pulmonaires/anatomopathologie , Veines pulmonaires/chirurgieRésumé
Thirty nine consecutive cases of congenital left ventricular inflow obstructions (LVIO) diagnosed by two dimensional and Doppler echocardiography are described. The commonest referral diagnosis was severe pulmonary arterial hypertension. Confirmation by cardiac catheterisation and/or surgery was available in twenty one of these cases. The ages ranged from one month to 15 years (mean 3.8 +/- 4.5 years) and 28 were males. Four types of LVIO were defined: i) Congenital mitral stenosis (22 cases). Ventricular septal defect was the commonest association. ii) Cor-triatriatum (7 cases) Out of three patients operated, in one it was found to be a supravalvular mitral ring and not cor-triatriatum as earlier thought on echocardiography. iii) Pulmonary venous obstruction (8 cases). Atrial septal defect and ventricular septal defect were the common associations. iv) Supravalvular mitral ring (2 cases). Double outlet right ventricle and a large ventricular septal defect were associated with one case each. In our experience, two dimensional and Doppler echocardiography is a very useful and reliable investigation for defining the various types of congenital left ventricular inflow obstructions and their hemodynamic significance.