Sujets)
Adulte , Enfant , Femelle , Humains , Mâle , Coeur foetal/chirurgie , Cardiopathies congénitales/chirurgie , Défaillance cardiaque/chirurgie , Transplantation cardiaque/méthodes , Transplantation cardiaque/normes , Brésil , Foetus , Cardiopathies congénitales/diagnostic , Défaillance cardiaque/congénital , Défaillance cardiaque/diagnostic , Appréciation des risques , Facteurs de risque , Sociétés médicalesRésumé
Heart failure (HF) is a complex syndrome, with several definitions, the commonest being "an abnormality of cardiac function whereby heart in unable to pump at a rate commensurate with the requirement of the metabolizing tissues, or does so only at elevated filling pressures". In case of children, this requirement includes growth and development. Unlike as seen in adults, HF in children is commonly due to structural heart disease and reversible conditions. Thus the treatment for HF is commonly required for short term only. The overall outcome with HF is better in children than in adults. While the general principles on management are similar to those in adults, the evidence for the use of drugs in children is less convincing. It requires a judicious balance of extrapolation from adult medicine, keeping in mind that children are not small adults.
Sujets)
Enfant , Défaillance cardiaque/congénital , Défaillance cardiaque/épidémiologie , Défaillance cardiaque/thérapie , Humains , PrévalenceSujets)
Nouveau-né , Humains , Cardiopathies congénitales , Cyanose/congénital , Sténose de la valve pulmonaire/congénital , Hypertrophie ventriculaire droite/complications , Hypertrophie ventriculaire droite/congénital , Hypertrophie ventriculaire droite/étiologie , Hypertrophie ventriculaire droite/génétique , Défaillance cardiaque/congénitalRésumé
Se informa el caso de un niño de seis años con cardiopatía congénita cianótica e insuficiencia cardiaca congestiva; al efectuar la autopsia, el corazón mostró características morfológicas de la anomalía de Ebstein con hipoplasia de la porción trabecular del ventrículo derecho. El desplazamiento distal del orificio tricuspídeo, con fusión de las valvas septal y posterior de la pared ventricular fue el criterio morfológico más útil para diferenciarla de otras cardiopatías que cursan con hipoplasia miocárdica del ventrículo derecho como la anomalía de Uhl, y la displasia del ventrículo derecho, entre otras cardiopatías secundarias. Se analiza el diagnóstico diferencial entre las anomalías que presentan ausencia parcial o difusa del miocardio del ventrículo derecho.
Sujets)
Humains , Mâle , Enfant , Maladie d'Ebstein , Dysplasie ventriculaire droite arythmogène/anatomopathologie , Défaillance cardiaque/congénital , Cardiopathies congénitales/anatomopathologieRésumé
A case of infantile hemangioendothelioma of the liver is reported in a 18 day-old male neonate. The neonate presented with CHF. He had hepatomegaly, but lacked the third component of the classical triad i.e. cutaneous hemangiomas. The S.A.F.P levels were raised to 920 ng/ml, though rise is rare in infantile hemangioendothelioma and led to the clinical diagnosis of hepatoblastoma. A left hepatic resection was performed, the histology showed a type I pattern of the tumor. This is known to be associated with a good prognosis. The baby is well post resection for a follow up period of six months.