Résumé
Eccrine syringofibroadenoma is a rare benign neoplasia derived from acrosyryngium cells of the eccrine sudoriferous glands. It affects the extremities of elderly individuals as solitary tumors, or may also present as multiple lesions. There are controversies about the pathogenesis and differentiation of the tumor. Eccrine syringofibroadenoma has been associated with subjacent conditions, such as for example, hypohidrotic ectodermic dysplasias. The authors describe a case report of a patient with Clouston Syndrome, who presented papules and nodules in extremities, clinically and histologically compatible with eccrine syringofibroadenoma. There are only three cases described in the literature, associated with Clouston Syndrome, and this is the fourth case.
Sujets)
Adulte , Femelle , Humains , Glandes eccrines/anatomopathologie , Dysplasie ectodermique/complications , Fibroadénome/complications , Tumeurs des glandes sudoripares/complications , Alopécie/anatomopathologie , Biopsie , Dysplasie ectodermique/anatomopathologie , Fibroadénome/anatomopathologie , Kératose palmoplantaire/anatomopathologie , Tumeurs des glandes sudoripares/anatomopathologieRésumé
Carney complex is an autosomal dominant disease that displays such characteristic features as cardiac and cutaneous myxomas and spotty pigmentation of the skin. We report here on a case of Carney complex that was accompanied by increased myxoid fibroadenomas in the breast and multiple intracranial aneurysms.
Sujets)
Adulte , Femelle , Humains , Tumeurs du sein/complications , Fibroadénome/complications , Anévrysme intracrânien/complications , Imagerie par résonance magnétique , Troubles de la pigmentation/complications , SyndromeRésumé
It is unusual for cysticercosis to occur in the substance of the breast. Only a few cases have been described in the literature. We report a case of cysticercosis perched on fibroadenoma of breast found on surgical excision in a 35 year old Nepali woman. The patient had no discernible evidence of cysticercosis in the other organs.
Sujets)
Adulte , Animaux , Maladies du sein/complications , Cysticercose/complications , Cysticercus/isolement et purification , Femelle , Fibroadénome/complications , HumainsRésumé
Los tumores benignos de la mama representan el 20 por ciento de las afecciones de la glándula y pueden desarrollarse sea a partir del tejido mamario específico, sea del estroma. De ellos el 70 por ciento corresponde a los fibroadenomas, el 10 por ciento a tumores papilares y el 9 por ciento a lipomas. Se analizan las características clínicas, semiológicas e histológicas de los principales tumores mamarios benignos, destacando entre ellos los fibroadenomas y los tumores papilares únicos y múltiples. Se mencionan también algunas lesiones poco freceuentes como la papilomatosis juvenil, el adenoma del pezón y el hamartoma. Se discute el valor de diversos porcedimientos actualmente disponibles en el estudio de los tumores benignos de la mama. Entre ellos destacan la mamografía, la ecotomografía, la biopsia con aguja fina y la citología por punción