Résumé
Se presenta el caso de un paciente masculino quien requirió tratamiento por agenesia anorrectal con fístula rectouretral y transposición pene-escrotal con hipospadias perineal, acompañados de una masa perineal. La tumoración perineal se encontró íntimamente adherida y en continuidad al recto, lo que la hace compatible con una duplicación rectal extrofiada. La reconstrucción quirúrgica de la anomalía se realizó en etapas hasta lograr resultados funcionales y estéticos aceptables.
We present the case of a male patient who required treaatment due to anorectal agenesis with recto urethral fistula and penoscrotal transposition with perineal hypospadias, associated with a perineal tumor. The perineal tumor was found strongly adhered and contiguous to the rectum which makes it compatible with an exstrophy of rectal duplication. Surgical reconstruction of the birth defect was performed in stages until acceptable biological function and esthetic results were obtained.
Sujets)
Humains , Nouveau-né , Mâle , Malformations multiples/anatomopathologie , Canal anal/malformations , Hypospadias/anatomopathologie , Pénis/malformations , Rectum/malformations , Scrotum/malformations , Malformations multiples/chirurgie , Cardiopathies congénitales/chirurgie , Hypospadias/étiologie , Hypospadias/chirurgie , Fistule rectale/congénital , Fistule rectale/étiologie , Fistule rectale/chirurgie , Maladies de l'urètre/congénital , Maladies de l'urètre/étiologie , Maladies de l'urètre/chirurgie , Fistule urinaire/congénital , Fistule urinaire/étiologie , Fistule urinaire/chirurgieRésumé
Congenital Penile Urethrocutaneous Fistula (CPUF) is an extremely rare anomaly. Commonly congenital urethrocutaneous fistulae are associated with anorectal anomalies and urethral duplication. The posterior urethra is the part, which is mostly affected. To the best of our knowledge, only 11 such cases have been reported so far in the English literature. A case of CPUF with a short review of literature.
Sujets)
Enfant d'âge préscolaire , Fistule cutanée/congénital , Humains , Mâle , Maladies de l'urètre/congénital , Fistule urinaire/congénitalRésumé
A 3-year-old male child was presented with the history of passage of urine coming from the undersurface of penis and its tip since birth. An opening was present on the ventral aspect of midshaft of penis through which a catheter could be passed. It was diagnosed as urethral fistula which was managed surgically.