Colecistectomía laparoscópica en situs inversus totalis / Laparoscopic cholecystectomy in situs inversus totalis

Situs inversus totalis es una anomalía congénita poco frecuente. Se caracteriza por la transposición de los órganos tóraco-abdominales en sentido sagital al brindar una imagen llamada en espejo. Reportamos paciente de 59 años con diagnóstico de litiasis vesicular y situs inversus totalis resuelto por colecistectomía videolaparoscópica, en el Hospital Universitario Comandante Manuel Fajardo de La Habana. El cuadro clínico tuvo seis meses de evolución, con dolor a tipo cólico en hipocondrio izquierdo acompañado de náuseas, que se relacionaban con la ingestión de alimentos colecistoquinéticos. Los exámenes de laboratorio estuvieron dentro de parámetros normales. La ecografía abdominal informó litiasis vesicular, así como, el situs inversus totalis que se confirmó con Rayos X de tórax. Su evolución posoperatoria, luego de un año, fue satisfactoria, la cual mostró la factibilidad de la técnica quirúrgica empleada(AU)

Situs inversus totalis (SIT) is a rare congenital anomaly characterized by the transposition of the thoracic-abdominal organs towards the sagittal direction, producing an image called in mirror. The case is presented of a 59-year-old female patient, with a diagnosis of vesicular lithiasis and situs inversus totalis for cholelithiasis, treated by laparoscopic cholecystectomy in Comandante Manuel Fajardo University Hospital of Havana. The patient's clinical picture had a natural history of 6 months, with left colic pain in the left hipocondrium, with nauseas, accentuated on ingestion of greasy meals. The laboratory test results showed normal parameters. X-rays of the abdomen confirmed vesicular cholestasis and situs inversus totalis. The patient's postoperative evolution after one year was satisfactory, showing the feasibility of the surgical technique used(AU)

Gorlin-Goltz syndrome with situs inversus: a rare case report / Síndrome de Gorlin-Goltz com situs inversus: relato de um caso raro

OBJECTIVE: To review the literature and present a case of Gorlin´s syndrome with situs inversus. RESULTS AND DISCUSSION: Together with the major features, a great number of processes considered as minor features have also been described in the Gorlin´s syndrome. The latter includes numerous skeletal, dermatology related and neurological anomalies among others. In the present clinical case many criteria allowed a diagnosis of Gorlin´s syndrome, but for the first time this unique finding of situs inversus is seen with this syndrome. CONCLUSION: However, further research is needed to confirm the association between situs inversus and Gorlin´s syndrome.

OBJETIVO: Revisar a literatura e apresentar um caso de síndrome de Gorlin com situs inversus. RESULTADOS E DISCUSSÃO: Conjuntamente com os aspectos principais, um grande número de processos considerados menores têm sido descritos na síndrome de Gorlin. Entre outras, numerosas anomalias esqueletais, dermatológicas e neurológicas têm sido relatadas. No presente caso clínico, muitos critérios permitiram o diagnóstico da síndrome de Gorlin, porém, pela primeira vez relata-se a ocorrência deste achado único, o situs inversus. CONCLUSÃO: Entretanto, pesquisas adicionais são necessárias para confirmar a associação entre situs inversus e síndrome de Gorlin.