Résumé
Intracranial sinus venous thrombosis (ICSVT) is a rare complication of ulcerative colitis that affects from 1.7 to 7.5% of patients. We report a 22 year-old male with ulcerative colitis in treatment with mesalazine and prednisone presenting with headache and speech disturbances. A magnetic resonance imaging of the brain showed a left temporal hemorrhagic infarct with thrombosis of the ispilateral superficial vein and sigmoid venous sinus. No cause of thrombophilia was detected. Anticoagulation with heparin was started which was changed to oral anticoagulation with warfarin. The patient was discharged ten days after admission.
Sujets)
Humains , Mâle , Jeune adulte , Rectocolite hémorragique/complications , Thromboses des sinus intracrâniens/étiologie , Anti-inflammatoires/usage thérapeutique , Anticoagulants/usage thérapeutique , Infarctus cérébral/diagnostic , Rectocolite hémorragique/traitement médicamenteux , Énoxaparine/usage thérapeutique , Céphalée/traitement médicamenteux , Céphalée/étiologie , Mésalazine/usage thérapeutique , Prednisone/usage thérapeutique , Thromboses des sinus intracrâniens/diagnostic , Thromboses des sinus intracrâniens/traitement médicamenteux , Troubles de la parole/traitement médicamenteux , Troubles de la parole/étiologieRésumé
A síndrome de Foix-Chavany-Marie (SFCM) caracteriza-se por apraxia da fala associada à paralisia bilateral da face, palato mole, língua e musculatura da faringe, mas com preservação das funções reflexas e automáticas. Na síndrome de Worster-Drought (SWD), há predomínio da disartria. Descrevemos o caso de uma jovem de 18 anos, que apresenta os achados clínicos e radiológicos compatíveis com a forma intermediária de SFCM/SWD, acompanhados de movimentos involuntários (coréia e distonia), fato de ocorrência rara na descrição destas síndromes.