IgG4-related disease manifesting with portal vein thrombosis : a case report - case report

IgG4-related disease (IgG4-RD) is a newly recognized disorder characterized by increased level of IgG4 and tumefaction or tissue infiltration by IgG4+ plasma cells.1,2 IgG4-RD can affect multiple organ systems. In this case report, we describe a patient who presented with portal vein thrombosis complicated with portal hypertension and esophageal varices. To our knowledge, this complication of IgG4-RD has not yet been described in the medical literature