RESUMO
We present a case of 49-year-old women with a huge intracranial chondrosarcoma. She had suffered from severe headache, nausea, vomiting and seizures for 2 months. Neurologic examination revealed left hemiplegia and bilateral blurred optic disc margins. Computed tomography scan and magnetic resonance imaging demonstrated a giant, heterogeneous, intensely enhancing mass of 7 x 8 x 6 cm, occupying the right parietooccipital regions parasagittal, with calcifications. A presumptive diagnosis of psammomatous meningioma or oligodendroglioma was made. The patient underwent right parieto-occipital craniotomy and total resection of the tumour. Pathologic examination revealed a chondrosarcoma. She was under regular follow-up and remained free of recurrence following surgery. In addition to the current case, we review previously reported cases of chondrosarcoma, discuss treatment strategies and outcomes