RESUMO
During 05 years period from January 2003 to December 2007, 45 cases of Ca. Pancreas were reported to LINAR and only one case of Pseudo Papillary Tumour of Pancreas is registered. It is a rare, low malignant potential pancreatic tumour. It has unknown pathogenesis and found in young females. We report a case of 24 years old female, who presented with pain in abdomen and low grade fever of 07 months duration. Lepratomy and excisional biopsy was done. H/P came as Pseudo Papillary Tumour of Pancreas. At presentation no any L.N. were found enlarged. Like other malignant pancreatic tumours, this neoplasm does not metastasize. Its definitive treatment is complete surgical removal, no any role of chemotherapy because it doesn't metastasize, limited role of radiotherapy in local invasive tumour or in residual mass