Congenital aortocaval fistula from right subclavian artery to superior vena cava in an adult with tetralogy of fallot

Congenital aortocaval fistula in association with complex congenital heart disease has never been described before. We represent an adult with tetralogy of fallot and an undiagnosed subclavian artery to superior vena cava fistula in previous catheterisms. He underwent surgical correction, successfully. After 8 months post operation he was doing well with improved functional capacity and no cyanosis

Multiple intussusceptions as primary manifestation of peutz-jeghers syndrome: report of a case

Peutz-Jeghers syndrome is a rare hereditary disorder characterized by hamartomatous polyps in the gastrointestinal tract and typical pigment lesions. It is a rare cause of multiple intussusceptions. Previous studies on Peutz-Jeghers syndrome reported only one case of multiple intussusceptions. We describe a case of appendiceal and multiple small intestine intussusceptions presenting as peritonitis in a patient with Peutz-Jeghers syndrome. A 17-year-old girl presented with an 8 day history of a sharp, non-radiating periumbilical pain. She underwent surgery with the diagnosis of peritonitis. Intraoperative findings included appendiceal and multiple small intestine intussusceptions. The final pathological evaluation of the specimen confirmed the diagnosis of Peutz-Jeghers syndrome. Multiple intussusceptions may occur as the primary manifestation of Peutz-Jeghers syndrome. Because of its complications, in view of the presence of multiple polyps, early intervention is strongly recommended