RESUMO
Tumors with skeletal differentiation [rhabdomyoma, rhabdomyosarcoma] and extra-renal rhabdoid tumors have been reported in uterus but cases of uterine leiomyoma with skeletal muscle like cells or cells resembling those of extra-renal rhabdoid tumors are rare. We describe clinical and pathological features of one such case of typical uterine leiomyoma in which histopathology showed presence of rounded, polygonal, and strap cells having abundant eosinophilic cytoplasm with round to oval nuclei, some of which were eccentric in position referred to as rhabdoid cells. Intra and extra-cytoplasmic hyaline globules were observed in these cells. However, no cross smooth muscle origin [positive for desmin and h-caldesmon while negative for cytokeratin, myogenin, myoglobin, and myo D1]. We also review the pertinent literature and emphasize that presence of such cells may lead to problems is important so that overtly aggressive management of a benign tumor is avoided