RESUMO
Posterior reversible encephalopathy [PRE] is a recent syndrome characterized by headache, vomiting, seizures, visual loss, altered mental status with or without motor or sensitive deficit. Neuroimaging demonstrates symmetrical posterior cortical and subcortical lesions. The aetiology remains uncertain but vascular hypotheses is the most retained. We report a case of a 21 year old man with posterior cerebral encephalopathy; the toxic hypothesis remains the most probable
Assuntos
Humanos , Masculino , Encéfalo/patologia , Encefalopatias/diagnóstico , Epilepsia , Imageamento por Ressonância Magnética , Vasoespasmo IntracranianoRESUMO
Epilepsy has been rarely reported with type 1 neurofibromatosis [Reckling Hausen disease]. It may occur in 3 to 6% of cases. We report in this study three cases of patients with type I neurofibromatosis associated with epilepsy. The patients were respectively 23, 30 and 35 years old. Epilepsy was focal and complex in one patient, generalized in one case and simply focal in another one. Cerebral MRI showed sphenoidal dysplasia and temporal lobe ectopy compressing orbital structures in one patient and normal in the other cases. We discuss through these three cases the relationship between Reckling Hausen disease and epilepsy