RESUMO
Background: Congenital hearing loss sensorineural variety is one of the most common birth defects. Imaging is very important to determine the underlying pathology of such cases
Objective: To assess the various cochlea vestibular bony and nerve anomalies by HRCT scan of temporal bone and MRI scan with 3D reconstruction images of inner ear
Methodology: A total of 140[280 ears] children with congenital deafness [88 males and 52 females], between 1 January 2012 to 30 September 2014 were included in this cross sectional study. All patients were assessed radiologically by HRCT scan of temporal bone and MRI with 3D scan of inner ear. This study was conducted at Al Razi Health Care Hospital, Lahore and Sheikh Zayed Medical College/Hospital, Rahim Yar Khan. The frequency of cochlear, vestibular aqueduct anomalies were noted. The data was entered an analyzed by using SPSS version 15
Results: We found various congenital anomalies of bony labyrinth and vestibulocochlear nerve in this study. Out of 280 inner ears we found 37 [13.2%] anomalous inner ears. Out of these 37 inner ears 25 [67%] has cochlear anomaly, 30 [83.1%] has anomalous vestibule, 19 [52.2%] has abnormal vestibular aqueduct and 9 [24.9%] has abnormal cochlea vestibular nerves
Conclusion: The study showed that most common ear anomaly in congenital sensorineural loss was cochlear vestibular, internal auditory canal anomalies. This study shows the outcome of preoperative inner ear assessment by radiological imaging mainly HRCTof temporal bone and MRI with 3D reconstruction