RESUMO
We report a 45-year-old man and a 60-year-old woman who presented with features of intermittent intestinal obstruction. Barium enema revealed narrowing at the pelvic-rectal junction in the man, and from the pelvic colon to the anal verge in the woman. Histology of the resected sections showed marked hypertrophy of the muscularis propria in both cases, with normal mucosa, submucosa and myenteric plexus. Both patients are asymptomatic at 4 years' and 2 years' follow up. This entity of primary hypertrophic colonopathy may be a variant of primary visceral myopathy.
Assuntos
Anastomose Cirúrgica , Colectomia/métodos , Doenças do Colo/diagnóstico , Feminino , Seguimentos , Humanos , Hipertrofia/complicações , Mucosa Intestinal/patologia , Pseudo-Obstrução Intestinal/diagnóstico , Laparotomia , Masculino , Pessoa de Meia-Idade , Doenças Retais/diagnóstico , Resultado do TratamentoRESUMO
Waldenstrom's macroglobulinaemia is a rare form of monoclonal plasma cell dyscrasia in which there is excess production of immunoglobulin M. Clinically the patient has features of hyperviscosity syndrome and the effects of bone marrow replacement by lympho-plasmacytoid cells. We report here two such cases seen within a period of two months.