A Case of Short Bowel Syndrome Due to Strangulated Congenital Internal Hernia in Children / 대한소아소화기영양학회지

Short bowel syndrome in children, most commonly results after extensive bowel resection for necrosis of the bowel. It may be caused by several intestinal catastrophes such as volvulus, hernia and necrotizing enterocolitis. The risk factors on short bowel syndrome are the remaining length of the bowel, the age of onset, the absence of the ileo-cecal valve and the time after resection. Macro and micronutritional deficiencies are the most significant complications of short bowel syndrome. We report a 5 year-old girl, who had a strangulated congenital transmesenteric hernia leading to short bowel syndrome accompanied by iron deficiency anemia.

The Comparative Study of Clinical Manifestations in Acute Poststreptococcal Glomerulonephritis with Gross Hematuria or Microscopic Hematuria

PURPOSE: This study aimed to compare the clinical outcome of acute poststreptocaccal glomerulonephritis (APSGN) between patients who had presented with gross hematuria and those with microscopic hematuria. METHODS: Thirty-nine patients with acute poststreptococcal glomerulonephritis, who were diagnosed from January 2000 to April 2003 were enrolled. RESULTS: The mean age was 8.85 years and the male to female ratio was 1.1:1. Seventeen patients presented with gross hematuria at diagnosis(group A) and twenty-two patients had microscopic hematuria only(group B). There were no significant differences between the two groups in the incidence of edema, fever or history of respiratory infection and oliguria. But hypertension was more frequent in group B. Laboratory data showed decreased C3 and C4 level in group B. Spot urine protein/creatinine ratio and 24hr urine protein showed higher levels in group A. CONCLUSION: Patients with gross hematuria at diagnosis had lower incidence of hypertension and a higher rate of nephrotic range of proteinuria than patients with microscopic hematuria. However, no difference in the duration of admission or complication rate was observed. All patients had clinical improvement during follow-up. We conclude that gross hematuria is not a significant prognostic factor for poststreptococcal glomerulonephritis.

Clinical Study of Kawasaki Disease in Infants 3 Months of Age and Younger

PURPOSE: The aim of this study was to describe the epidemiological pictures and clinical profiles of Kawasaki disease(KD) in infants 3 months and younger. METHODS: For the epidemiologic study of KD in Korea as a task of Korean Pediatric Cardiology Society, data of total 3,862 KD patients were collected from 1997 to 1999 by survey. Among them, clinical data of 71 KD patients aged 3 months and younger were analyzed and compared with those of the total KD patients group. RESULTS: 71 patients aged 3 months and younger(1.8% of total 3,862 KD patients) included 1 case aged under 1 month, 22 cases aged 1-2 months, and 48 cases aged 2-3 months. The male-to-female ratio was 1.96:1, and the recurrence rate was 1.4%, and the prevalence of cases in sibling was zero. Coronary arterial (CA) abnormalities were detected by echocardiography in 27.5% of the cases, including 10.1% of CA aneurysm cases. There were no case with myocardial infarction or death. CONCLUSION: Comparing with the data of total KD patients group, data from 71 patients aged 3 months and younger showed a somewhat higher male-to-female ratio, incidence of CA abnormalities, and incidence of CA aneurysms, however those had no statistical significance.