Extrarenal Wilms' Tumor in the Retroperitoneum: A Case Report / 대한소아혈액종양학회지

Extrarenal Wilms' tumor is an extremely rare solid tumor in childhood. The most common location is the retroperitoneum or inguinal area. The diagnosis should be made by histologic confirmation of Wilms' tumor of extrarenal origin and by excluding the existence of supernumerary kidney or embryogenic tumor with teratomatous components. We report a 4 year-old boy with retroperitoneal extrarenal Wilms' tumor, considered to be the second case reported in Korea, who has been relapse-free for 26 months after the completion of chemotherapy. We also made a brief review of the literatures.