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Rev. argent. dermatol ; 90(3): 152-164, jul.-sep. 2009. graf, tab
Artigo em Espanhol | LILACS | ID: lil-634388

RESUMO

Antecedentes: los tumores anexiales cutáneos representan un grupo heterogéneo de entidades de baja frecuencia de presentación, que puede plantear ciertas dificultades diagnósticas para el patólogo general. Métodos: se realizó un estudio retrospectivo observacional, revisándose informes cuyo diagnóstico correspondía a tumores anexiales, realizados en la institución entre los años 2000 y 2007. Se utilizó la clasificación de tumores anexiales de la WHO del consenso del año 2003 en Lyon. De dichos informes, se registraron características como género y edad, localización, histopatología, márgenes y multicentricidad, entre otras. Resultados: fueron recolectados 200 informes correspondientes a 178 pacientes, encontrándose en 13 de ellos más de un tumor. El 50% era de sexo masculino. El 47% correspondía a tumores foliculares, el 42% a tumores ecrinos y apócrinos y el 11% a tumores sebáceos. El más frecuente de los tumores foliculares fue el pilomatrixoma (67%); entre los ecrinos y apócrinos, el siringoma (24%) y de los sebáceos se destacó el carcinoma (63%). El 84,5% correspondía a tumores benignos, el 12% a malignos y el 3,5% a tumores de potencial incierto. Entre los tumores ecrinos y apócrinos, se registró un predominio del sexo femenino y en los restantes del sexo masculino. Los tumores foliculares se presentaron a edades más tempranas y los sebáceos, a edades mayores. Todos ellos se localizaron principalmente en la región cefálica. Conclusión: nuestros resultados demostraron concordancia con la literatura consultada y confirmaron la heterogeneidad de dichos tumores en su presentación como biopsias cutáneas, a pesar de su baja frecuencia.


Introduction: skin´s adnexal tumors represent a heterogeneous group of lesions of low frequency of presentation, which can cause certain diagnostic difficulties for the general pathologist. Materials and methods: a retrospective study was carried out. The reports about adnexal tumors performed in the institution between the years 2000 and 2007 were revised. The Who classification of adnexal tumors from the consensus of 2003 in Lyon was used. The gender, age, localization, histopathology, margins and other characteristics of the biopsies were revised. Results: 200 reports were revised corresponding to 178 patients. 13 of them presented more than one tumor. 50% were men. Among all the reports, 47% corresponded to follicular tumors, 42% to apocrine and eccrine tumors and 11% to sebaceous tumors. Between the follicular ones, the pilomatricomas were the most common (67%), among apocrine and eccrine ones, were the syringomas (24%) and the sebaceous carcinomas (63%) were the principal diagnostic as regard sebaceous tumors. 84.5% were benign, 12% were malignant and 3.5% were of uncertain biological potential. There was a female predominance between the apocrine and eccrine tumors. The sebaceous and follicular tumors were more common in men. The follicular ones were diagnosed in earliest ages, in contraposition with the sebaceous ones, diagnosed in advanced ages. All of these tumors were more frequent in cephalic region. Conclusions: our results showed concordance with the literature and confirmed the heterogeneity of these tumors in their presentation as skin biopsies, in despite of their low frequency.

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