RESUMO
Paciente de 16 anos, sintomática, encaminhada com suspeita de coartctaçäo da aorta clássica. O estudom hemodinâmico revelou grave coarctaçäo da aorta logo após a artéria subclávia esquerda e grande aneurisma da regiäo pós-estenótica. Correçäo cirúrgica com retirada "em bloco" do aneurisma foi realizada com sucesso e dois meses após a cirurgia a pressäo arterial da paciente estava normal e o aspecto ecodopplercardiográfico era bom, com gradiente de 10/mmHg no local da anastomose
The case of a symptomatic 16-year-old girl, referred with the diagnosis of coarctation of the aorta is presented. Aortography showed a severe coarctation and a huge aneurysm distal to the coarctation. Successful operation was performed with resection of the coarctation and aneurysm and interposition of a tube of bovine pericardium for the anastomosis. Two months after the operation the blood pressure was normal and a 10mm/Hg gradient was detected by dopplerechocardiography