Primary leiomyosarcoma of the mandibular alveolus - a rare entity

The primary Leiomyosarcoma of the mandibular soft tissue is an extremely rare tumour. A review of literature since 1908 shows only 6 reported cases. We are reporting another case of primary Leiomyosarcoma of the oral cavity in a child 6 years of age, who presented with a painless swelling in the oral cavity involving the left lower alveolus. The diagnosis was established by histopathology and immunohistochemical studies. The patients was treated surgically by wide excision and clearance of the primary site, i.e. segmental mandibulectomy, along suprahyoid neck dissection