A case of varicella induced remission of nephrotic syndrome

Here authors report a case of a 7-year old girl diagnosed with nephrotic syndrome with urinary tract co-infection who during treatment with steroids developed a Varicella Zoster infection. After cessation of steroid therapy and commencement with antiviral drugs, the patient showed significant reduction in nephrotic features and complete resolution of nephrotic syndrome as with the VZV super-infection.

Severe generalized dystonia in paediatric onset wilsons disease

Wilson disease (WD) is a rare autosomal recessive disorder with defect in copper transport mechanism with varied clinical manifestation predominantly hepatic, neurological, ophthalmological and multi-systemic involvement. WD in paediatrics' age group manifest differently from the adults.' In this case report, Authors have' described the first case report presenting with neurological involvement in the form of severe generalized dystonia in a paediatric onset WD. This case report is of greater significance in detecting the most often undetected paediatric WD presenting with a usual hepatic manifestation occurring early in the course.