RESUMO
@#Aggressive Angiomyxoma is a rare, slow growing, benign mesenchymal tumor arising from the pelvis and perineum which commonly affects women in the reproductive age group. Though benign, it is locally infiltrative with a marked tendency for local recurrence. We report a case of aggressive angiomyxoma of the vulva with translevator extension into the pelvic cavity in a 33 year old G2P2(2002). She presented with a left labial mass that recurred two years after excision was done. Debulking of the mass was carried out by abdominal and perineal approach. Histopathologic studies of the mass confirmed aggressive angiomyxoma. Long-term periodic follow-up with imaging studies was advised because of its high rate of recurrence in spite of negative tumor margins after wide excision