Congenital umbilical appendix

We report a case of a 3 years old female with umbilical appendix presenting with a fistula. Initial examination, which was done by a midwife, missed a congenital appendix protruding through the umbilicus. Ligation of this cord resulted in fistula formation. The patient was successfully managed by doing an appendectomy. Congenital umbilical anomalies are rare, only handful of cases have been reported so far. Most umbilical neonatal anomalies described in literature are derived from the vitelline duct. In this article we describe the clinical presentation and management of an umbilicus appendix presenting with a fistula following umbilical cord ligation. We also review the embryological origin, and aetiological facors