RESUMO
Chondrosarcoma (CS) is a malignant tumor of long and flat bone characterized by the formation of cartilage. Mesenchymal chondrosarcoma is a rare variety of chondrosarcoma .It is a biphasic tumor with areas of spindle cell mesenchyme along with chondroid differentiation in the connective tissue stroma. A 17 year old male presented to us as a painless mass in maxilla. Contrast enhanced computed tomography (CECT) showed a lytic expansile lesion in the right maxillary bone with foci of calcification within soft tissue lesion. Fine needle aspiration cytology (FNAC) and incisional biopsy was performed which confirmed the diagnosis of maxillary Mesenchymal chondrosarcoma .The patient underwent right subtotal maxillectomy with 2 cm margins. The review of literature shows that very lesser number of maxillary Mesenchymal chondrosarcoma cases were reported so far. Therefore an attempt is made to add this rare case of MC of maxillary alveolus in the Existing literature.