RESUMO
A childhood case of moyamoya disease with subarachnoid hemorrhage is reported. This patient exhibited left hemiparesis, dysarthria, convulsion and mental retardation. He also had characteristic angiographic picture: occlusion of supraclinoid segment of both internal carotid arteries, combined with collateral networks in the base of brain.
Assuntos
Criança , Humanos , Encéfalo , Artéria Carótida Interna , Disartria , Deficiência Intelectual , Doença de Moyamoya , Paresia , Convulsões , Hemorragia SubaracnóideaRESUMO
Cushing's syndrome is a rare entity in pediatric age, and and mostly caused by adrenocotical tumor. We recently experiecd 2 cases of Cushing's syndrome, one, 13 year and 4 month old girl with bilateral adrenocortical hyperplasia, and one, 2 year and 4 month old girl with huge adrenocortical carcinoma measuring 14x13x8cm, thought to be congenital in origen. The former was successfully treated by bilateral adrenalectomy. The latter showed no evidence of metastasis at operation, but expired 7 months later due to metastatic carcinoma. Literature about Cushing's syndrome were reviewed.