[Percutaneous bile drainage: complications and efficiency at short and mean terms: about 50 cases]

Our purpose is to evaluate the efficiency and mean term complications in percutaneous bile drainage through a retrospective study of 50 cases :Fifty patients aged from 24 to 87 years underwent perecutaneous bile drainage in the Radiology Department of Mongi Slim hospital. Patients had external drainage, internal drainage or endoprotheses. Clinical and biological features were used to evaluate efficiency and complications. Bile drainage was successful in 49 cases. Intra hepatic bile ducts were dilated in most of the cases [40 patients]. A right lobe puncture was performed preferentially [41 patients]. Fifteen patients had endoprotheses, 3 patients had internal drainage and 31 patients had external drainage. Clinical and biological improvement was noted in all patients. Complications were noted in 16 cases mainly in patients with neoplastic obstruction. Percutaneous bile drainage is an effective method for the treatment of biliary obstruction. Complications are rare, occurring most frequently in patients with neoplastic obstruction

novel mutation in infant hypophophatasia: a case report

Hypophosphatasia is a rare inherited disorder characterized by defective bone and teeth mineralization and deficiency of serum and bone alkaline phosphatase activity. Several mutations in the TNSALP gene are identified. The authors describe a Tunisian case having a mutation that has not been described up to now. It is about an infant, in the antecedents of recurring disease of the lungs in child since the age of seven months, which presents clinical and radiological signs of rickets. The diagnosis of hypophos-phatasia is strongly suspected in front of Reduced serum alkaline phosphatase activity and confirmed by the genetic study. The child is homozygous for a new mutation L282P in the ninth exon of the gene. The parents and two brother and sister are heterozygous for the same mutation

Leucoencephalite aigue du nourrisson traitee par fortes doses de corticoids

The authors report a case of acute post infectious leukoencephalitis observed in a two-years and a half child admitted to our hospital for fever with sudden condition deterioration, obnibulation, coma and paralysis of the 6th and 7th cranial nerve. Cerebrospinal fluid study showed lymphocytosis with negative culture. Head magnetic resonance imaging demonstrated diffuse high signals over the white matter on T2 weighted images so the diagnosis was confirmed. High dose corticosteroid therapy was effective

Arthropathie de Jaccoud et chondrocalcinose articulaire: Une association rare

Jaccoud's arthropathy [JA] is a chronic deformity affecting hands and feet, which are voluntarily correctable by the patients. JA was usually reported in assocation with rheumatic fiver and systemic lupus erythematosus. We describe an exceptional association between a pyrophosphate arthropathy and JA of the hands. It is a 48 year old woman, having a 13 years history of polyarthritis involving shoulders, elbows, hips and knees, and 4 years after, a progressive under deviation of the fingers of the hands. Calcium pyrophosphate dihydrate crystals were identified in the synovial knee biopsy. Hands xrays as RMI don't identify erosions and confirmed the JA

Diagnostic echographique de l'acranie: Malformation embryologique rare

The authors reports a case of acrania diagnosed on antenatal period in a routine morphologic ultrosonography at 19 weeks of intra uterine gestation on a 20-year-old patient, gravida 1, para 0. Acrania associafed with exencephly is a rare and lethal maltormation characterized by a defect of developpement of the flat bones of the scalp whereos cerebral tissue is present often abnormal. Ultraisonography had allowed to find besides the cerebral malformation, spinal and visceral fetal molformations as well as cord abnormality that included only two vessels