[Nevus lipomatosus cutaneous giant of hoffmannn zurhelle a case report]

Nevus lipomatosus cutaneous superficialis [NLCS] of Hoffmann-Zurhelle is a rare hamartomatous skin lesion histologically characterised by the presence of mature fat tissue within the dermis. Clinically, two types of NLCS are distinguished: a multiple type and a solitary type. Illustration of anatomoclinical presentation of this rare lesion and the hypothesis of its pathogenesis. We report a case of a NLCS diagnosed in a 16-year-old girl, which was exceptional by its huge volume. This lesion was localised in the right thigh. The patient underwent wide excision of the mass without complication. The tumoral form is rarely reported in the literature, and its pathogenesis is unknown