RESUMO
Familial haemophagocytic lymphohistiocytosis [FHL] is a rare genetic disease, typically occurs during infancy and early childhood and is fatal in 1-2 months from presentation if not diagnosed and appropriately treated. The dramatic clinical presentation with multisystem involvement is described in our typical case. Early diagnosis and treatment offers this child a good chance of prolonged remission and possibly cure. As this condition is frequently not diagnosed, with dire consequences except we describe our case to increase awareness and improve the outcome for others
RESUMO
The Paediatric Oncology Unit in Tawam Hospital was established in 1983 as the United Arab Emirates [UAE] referral center for childhood cancer. The activity, scope and success of the unit have increased over the years. To review the types of cancer seen and relative frequency, patient demographics, and the success rate for children treated here compared to other centres. A survey was undertaken of all cases of paediatric cancer during the 7-year period from January 1995 to December 2001