RESUMO
Pancreaticobiliary maljunction (PBM) is a congenital disease with pancreatic and bile ducts joining outside of the duodenal wall. The clinical symptoms of PBM are often characterized by a series of gallbladder and pancreatic disease. PBM has also gradually drawn attention due to recurrent of pancreatitis, bile duct stones and the malignant tumors of biliary system. With the innovative development of endoscopic minimally invasive technology, therapeutic endoscopy may provide new treatment options and ideas for PBM patients, and is expected to achieve the goal of endoscopic minimally invasive intervention to correct structural abnormalities in the pancreaticobiliary duct junction. This paper provided an overview of the definition, endoscopy diagnosis, the pathogenesis and therapeutic endoscopy progress of pancreaticobiliary maljunction.