[Immunological aspects of the kidney transplantation]

The immunological rejection is still, at the present time, a major risk in kidney transplantation. Accurate assessment of the immunological status of all patients awaiting transplantation or grafted, can assess this risk, this work is intended to describe, in the framework of kidney transplant from living donor, the role of the laboratory of histocompatibility in the immunological care and monitoring of patients: pre-transplant analysis, limitations and performance of available analysis techniques, criteria for matching pairs donor/recipient, follow-up of immunological post transplant. The last part will be devoted to the experience of the immunology unit at the blood transfusion service of ibn Sina Hospital in Rabat

Kartagener syndrome: a case report

The Kartagener's syndrome is a rare autosomal recessive disease. The diagnosis is based on the associated of nasal polypose, dilatation of branches and situs inversus. The authors report a case of a 45 day-old girl, admitted for broncho-pneumonia with deviation of heart noises to the right. The cardiac and abdominal scan finds a complete situs inversus. Our patient was treated by antibiotherapy and daily respiratory physiotherapy. The outcome was good. The aim of this case report is to remind a diagnosis which is very uncommon in this context, and to study epidemiology, clinical, therapeutic and evolutive characteristics of this disease

[Wolman disease: a case report]

The Wolman disease is a rare autosomal recessive disorder associated with reduced activity of lysosomal acid lipase [LAL] witch leads to the tissue accumulation of cholestryl esters and triglycerides. The authors report a case of 3 month-old infant who was admitted for abdominal distension with hepato-splenomegaly, diarrhea, vomiting, anemia and inanition. The diagnosis was made on the radiological evidence of bilateral adrenal calcifications. The patient died during the first 3 months of life. It is recommended that plain abdominal X-Ray must be obtained to check for the typical pattern of adrenal calcification in any young infant with evidence of a storage disease without dysmorphic features