RESUMO
A crantocervial junction neurenteric cyst as a cause of bulbomedullary compression, is a very rare lesion. A failure during the third week of the embryogenesis may be responsible for its formation. A 38-year-old man displayed a progressive right hemiparesis associated wrth lower cranial nerve disorders, and acute bladder retention. Magnetic resonance imaging demonstrated an intradural extramedullary process of the craniocervical junction. Surgical posterior approach allowed a gross total resection of the lesion. Histological examination of the surgical specimen showed that the cyst wall consisted of fibrocollagen walls lined by partially ciliated columnar epithelium. In the postoperative course, clinical signs resolved completely Patient was symptom free after 2 years follow-up. The posterior surgical approach was safe and allowed a complete removal with a good long-term outcome. Early surgical removal is the therapy of choice