Wegener’s granulomatosis: Is it rare?

A 52 year old lady was admitted with fever, productive cough and breathlessness for one month. She had past history of recurrent sinusitis. Clinically, she had bilateral sensorineural hearing impairment, nasal crusts and peripheral neuropathy apart from signs of consolidation. Vasculitic lesions appeared a day after admission. Investigations revealed multiple nodular like lesions scattered in both lungs on CXR. Blood tests revealed positive cANCA (Cytoplasmic fluorescence Antineutrophil Cytoplasmic Antibodies) and raised infl ammatory markers. She was treated with immunosuppressant and antibiotic. Clinical and radiological improvement was noted 2 weeks later.