Isolated Congenital Tracheobiliary Fistula

Background: Congenital tracheobiliary fistula is a rare developmental anomaly with apersistent communication between the biliary system and the trachea. Characteristics: A7-day-old baby with severe respiratory distress and aspiration pneumonia. Outcome:Tracheobilliary fistula identified on bronchoscopy. Open surgical excision of fistula wasfollowed by improvement. Message: This condition should be considered in the differentialdiagnosis of intractable aspiration pneumonia.