RESUMO
Introduction: Adenomatoid odontogenic tumor (AOT) is a rare epithelial odontogenic tumor of jaws. It is a benign, painless, non-invasive, slow-growing lesion, with a frequency of 2.2-7.1%. Upon clinical examination it can be misdiagnosed as an odon- togenic cyst. AOT affects young individuals with a female predominance, occurs mainly in the second decade, more common in anterior maxilla and usually surrounds the crown of unerupted tooth mostly impacted canine. AOT has three clinical subtypes named as follicular, extrafollicular, and peripheral. Clinical presentation: This case report represents a 20 years old female patient with the chief complaint of swelling on the right upper anterior region for 8 months. Management and prognosis: After surgical excision and histopathological evaluation it is diagnosed as a rare case of extrafol- licular variant of intraosseous AOT.