Pattern of cutaneous disorders in the South Eastern Iran, Kerman

To identify the pattern of common cutaneous disorders in the region of South Eastern Iran, Kerman Province. In this study, 1000 patients who had been referred to the Afzalipour hospital clinic during a three months period in the autumn of 2013 were included. Excluding those who had repeat visits, 900 new cases were detected including multiple diagnoses in some patients. Dermatology residents analyzed the medical records of the patients [history, physical examination and laboratory investigations]. The diagnoses were classified according to WHO International Classification of Diseases, revision [ICD 10]. Descriptive statistics were used to analyze the data. There were 500 male [55.5%] and 400 female [44.5%] patients and the mean age of the patients was 30.7 +/- 6 years. Among the non-infective diseases, dermatitis and urticaria [31%] were the most common cutaneous disorders for attendance, followed by infectious diseases [19%], pigmentary diseases [15%], acne vulgaris [14%], papulosquamous diseases [10%], out of which psoriasis contributed to 45 [5%] cases. Hair diseases [3%], skin tumors [2.2%], nail diseases [2%], adverse drug reactions [2%], vesiculobullous diseases [1%] and cutaneous manifestations of systemic diseases [0.8%] contributed to the rest of cases. The management of the vast majority of cases [85%] consisted of advice with a prescription, while only [5%] of patients required admission. Dermatitis and skin infections were the most common cutaneous disorders in our study population. On the basis of the present data, improving the socio-economic status, environmental and personal hygiene, as well as, specific instructions to the risk group can be beneficial

Elejalde syndrome: case presentation

Silvery hair and severe dysfunction of the central nervous system [Neuroectodermal melanolysosomal disease or Elejalde Syndrome] characterize this rare autosomal recessive syndrome. Main clinical features include silver-leaden hair, bronze skin after sun exposure, and neurologic involvement. Large granules of melanin unevenly distributed in the hair shaft are observed. Abnormal melanocytes and melanosomes and abnormal inclusion bodies in fibroblasts may be present. We report a 10-year-old girl with a silver-leaden [silvery] hair, bronze skin color on sun-exposed areas, generalized hypopigmentation of covered body parts and congenital seizures. The child was the elder of two children born of a consanguineous marriage. The younger sibling, a female neonate, had same clinical presentation

Bullous ichthyosiform erythroderma: case presentation

Bullous Ichthyosiform Erythroderma [BIE] is a rare disorder of keratinization [mutation in either keratin 1 or 10]. It typically presents with fragile skin, which gives way to gradual evolution of hyperkeratosis. Flaccid blisters, peeling and superficial erosions at sites of minor trauma or friction are apparent within the first few hours of life. Yellow-brown, waxy, ridged or corrugated scale builds up in skin creases, sometimes forming spiny [Hystrix] outgrowths. Cobblestone-like keratoses occur at other sites such as the dorsal hands and feet and over the trunk. We report an 11-year-old boy with a generalized hyperkeratosis on the neck, trunk, extremities and scalp