Hematologic abnormalities in cyanotic congenital heart disease patients

Introduction: Patients with cyanotic heart disease may have an acceptable quality of life. However, they are invariably prone to several complications. The aim of this study is search about hematologic abnormalities in cyanotic congenital heart disease patients

Materials and Methods: In this cross-sectional study, every cyanotic congenital heart disease patients who was referred to the adult congenital heart disease clinic was selected and asked of any possible hyperviscosity symptoms, gingival bleeding, epistaxis, hemoptysis, hypermenorrhagia, and gouty arthritis irrespective of their age, gender and primary diagnosis in a six-month period. In this regard, 02 saturation was obtained via pulse oximetry, an abdominal ultrasound was done in order to discover any gallstones and laboratory tests including CBC, coagulation parameters [bleeding time[BT],clotting time[CT], prothrombin time[PT],international ratio[ INR], Ferritin, blood urea nitrogen [BUN] and creatinine [Cr] were provided as well

Results: A total of 69 patients were enrolled in the present study. The mean age of the patients was 22.44 +/- 5.72. Twenty two [34.4%] of them were female and 45[65.6%] were male. In our research, 23% of the patients had serum levels of uric acid more than or equal to 8 mg/dl. 59%of patients presented with depleted iron storage. Mean hemoglobin [Hg], level was [16.9 +/- 2.5 mg/dl], mean hematocrit [HCT] level was [55.47 +/- 9 mg/dl], mean Ferritin level was [32.5 +/- 0.4]. Our collected data also revealed that plasma creatinine concentration was normal [0.9 +/- 0.2 mg/dl]. Furthermore, thrombocytopenia of less than 160000 was found in 30% of the patients. Hyperviscosity symptoms also found in 1.3% of patients

Conclusion: Our patients had less hyperuricemia, there is no correlation between hyperviscosity symptoms and haematocrit level and an inverse correlation between the Ferritin level and hyperviscosity symptoms were seen

An Unusual Biatrial Cardiac Myxoma in a Young Patient

This is a report of a biatrial cardiac myxoma in a young man with a 10-month history of exertional dyspnea and palpitation. The echocardiogram revealed biatrial myxoma prolapsing through the mitral and tricuspid valves during diastole. All cardiac chambers were enlarged and dysfunctional. The electrocardiogram revealed a rapid ventricular response with atrial flutter rhythm. The masses were resected and diagnosed as myxoma by a histological examination. The follow-up echocardiogram revealed significant improvement in ventricular function and reduction in the cardiac chambers' volume. There was no evidence of myxoma recurrence. The most probable cause of the patient's heart failure was considered to be tachycardia-induced cardiomyopathy.

Congenital aortocaval fistula from right subclavian artery to superior vena cava in an adult with tetralogy of fallot

Congenital aortocaval fistula in association with complex congenital heart disease has never been described before. We represent an adult with tetralogy of fallot and an undiagnosed subclavian artery to superior vena cava fistula in previous catheterisms. He underwent surgical correction, successfully. After 8 months post operation he was doing well with improved functional capacity and no cyanosis