A Nutritional Study of Tube-fed Patients with Severe Neurodevelopmental Disability / 대한소아소화기영양학회지

PURPOSE: The purpose of this cross-sectional study was to assess the nutritional states and investigate the energy intake of tube-fed patients with severe neurodevelopmental disability. METHODS: Eighty six tube-fed patients with severe neurodevelopmental disability were studied. Heights were measured by flexible scale segmentally. Nutritional parameters of weight, triceps skin- fold thickness and mid-arm circumference were also measured. Total caloric intakes through the tube were calculated. RESULTS: The anthropometric results showed that nutritional states of tube-fed patients with severe neurodevelopmental disability were poor. The mean daily caloric intake was much less than daily energy requirement (mean=45.2% of requirement). The caloric intake was 7.2 kcal/height (cm), 57.0 kcal/weight (kg). Height was more related with caloric intake (r=0.476) than weight (r=0.263). CONCLUSION: These results provide that tube-fed patients with severe neurodevelopmental disability were growth retarded and their energy intakes were much less than daily energy requirements. The preliminary evidence was that they need adequate nutritional supply.

A Case of Mucocutaneous Lymph Node Syndrome Complicated by Aseptic Meningitis, Hydrops of the Gallbladeder and Dilatation of the Coronary Arteries

No abstract available.

Statistical Observation for Pediatric Inpatients

No abstract available.

A Case of Acute Febrile Mucocutaneous Lymph Node Syndrom Complicated with Ileus

No abstract available.

A case of Thrombasthenia

A 6 year 6month-old boy was admitted with complains of severe spontaneou epistaxis and easy brusability. He was one of five siblings, and two of them died of recurred severe epistaxis at their age of six years. There was no history of bleeding tendency to his antecedents and parents, whose marriage was unrelated. Platelet count and partial thromboplastin time were noraml with prolonged bleeding time, but clot retraction was poor. Platelet adhesion(Salzman method) was decreased and platelet aggregation test showed flat curve with no response to epinephrine and ADP. These tests of other were normal. Diagnosis of thrombasthenia was made with the above history and laboratory results.

A case of Thrombasthenia

A 6 year 6month-old boy was admitted with complains of severe spontaneou epistaxis and easy brusability. He was one of five siblings, and two of them died of recurred severe epistaxis at their age of six years. There was no history of bleeding tendency to his antecedents and parents, whose marriage was unrelated. Platelet count and partial thromboplastin time were noraml with prolonged bleeding time, but clot retraction was poor. Platelet adhesion(Salzman method) was decreased and platelet aggregation test showed flat curve with no response to epinephrine and ADP. These tests of other were normal. Diagnosis of thrombasthenia was made with the above history and laboratory results.

A Clinical Study of 15 Cases of Pneumocystis Carinii Pneumonia

No abstract available.

A Clinical Observations on Childhood Bronchial Asthma

The results of clinical observation and intradermal test on 44 bronchial asthma patients who were seen at the department of pediatrics, N.M.C. fro Jan. 1967 to Jun. 1979 were presented. 1) Age distribution at the time of admission ranged between 2 years and 14 years. Most of the patients(70.5%) were between 4 and 9 years of age. Sex ratio was 2.1:1 with male predominance. 2) The peak age of the onset was between 3 and 6 years of age, 30 cases being included. 3) In 30 percent of the cases there noted allergic history other than asthma. Allergic family history was positive in 30 %. 4) Seasonal variation showed peak incidence in fall followed by summer, winter and spring in order. The perennial attacks include 9.1% of the cases. 5) Eosinophilia was noted in 64.1% and closely related to the allergic history of the patient. 6) On chest x-ray findings, 28.6% were normal, 40.5% had infiltration and 31.0% were emphysematous. 7) Intradermal tests were performed on 10 parients. All of the them showed positive reaction and total frequency of detection of allergens revealed more than 2. 8) Allergens with positive reactions were dust in 90%, animal hair in 70%, foods in 60%, mold in 50% and pollen in 10%. 9) All the patients were reactive to medical treatment, with complete relief of symptoms in 81.89% and incomplete relief in 18.2%. No morality was noted.

A Clinical Observation on Neonatal Bacterial Meningitis

Neonatal bacterial meningitis remains as one of the significant causes of death and neurological sequellae. Twenty four cases of neonatal meningitis who were admitted to pediatric department, National Medical Center from Jan. 1970 to Dec. 1978 were reviewed clinically and the following results were obtained. 1. Age of onset was chiefly in the lst week of life(57.4%) followed by the 2nd week of life(25%). 2. Sex ratio showed predominance of male(83.3%). Seasonal distribution was non remarkable. 3. Among 24 cases, there noted 11 cases of positive cultrues for the etiologic agents, 5 of Gram positive and 6 of Gram negative. 4. Mean duration of days between the onset and the diagnosis was 2.5 days. The most common presenting symptoms and signs were poor sucking, irritability and lethargy. 5. On cerebrospinal fluid examination there noted increased cell count and protein and decreased sugar content in all cases 6. Case fatality rate was 25%. Subdural effusion was complicated in 20% of the cases but no hydrocephalus was noted.

A Case of Chronic Granulomatous Disease (Autopsy case)

A 3 year and 3 months old boy with recurrent infections since his age of 5 months was presented with clinical data and autopsy findings. He was the 4th product of healthy parents. His elder brother died of recurrent perianal abscess and sepsis at his age of 3 years. His 2nd elder sister died on the 14th day of life probably from the complication of BCG vaccination. Beginnig with perianal abscesses at his age of 5 months, he has been continuously suffering from recurrent infections such as arthritis, ostomyelitis, pneumonia, epididymitis, subcutaneous abscesses and perianal abscesses. In spite of meticulous supportive and aggressive antibiotic therapy persistent positive cultures for staph. Aureus, klebsiella, E. Coli, Enterococcus and coliform bacilli from different sited were noted. Erythrocyte sedimentation rate of 25 to 40 were constant. White cell count varied frem 15500 to 33400 with polymorphonucleocytes predominance. NBT test showed persistent low scoring of 2% throught the course. He finally died of pneumonia and empyema. At postmortem examination, multiple abscesses and grnulomas of right lung and multipe granulomas in the liver, spleen, lymph node, bone, marrow, adrenal gland, kidney and intestinal wass were noted. At microscopic examination histiocytic granulomas with lipid containing histiocyte infiltrations were noted in every organs described including brain.