Anodontia of permanent teeth - a case report

Anodontia is a rare genetic disorder which represents the congenital absence of all teeth in primary, permanent or both dentitions. Anodontia is usually a part of a syndrome and seldom occurs as an isolated entity. It is commonly associated with complex pathology known as Ectodermal dysplasia which originates from the abnormalities during the early stages of embryonic development, and usually transmitted as an X- linked recessive disorder. In this report a case of 10 year old boy is presented who had complete set of primary dentition except maxillary lateral incisors, but surprisingly complete absence of permanent dentition in radiological observation. In this case, anodontia is not associated with any syndrome which is a rare finding